What is Idiopathic Pulmonary Fibrosis?

What is IPF?

Idiopathic pulmonary fibrosis (IPF) is a serious chronic disease that affects the tissue surrounding the air sacs (alveoli) in the lungs.

Progressive scarring

IPF is characterised by progressive scarring (fibrosis) of lung tissue, which makes the lungs stiff and less able to function properly.

Unknown cause

The term "idiopathic" means the cause is unknown. While smoking and genetics are associated with IPF, the exact trigger for the disease remains unclear.

Affects older adults

IPF typically affects people between the ages of 50 and 75.

Shortness of breath and cough

The most common symptoms of IPF are shortness of breath, particularly during exertion, and a dry, hacking cough.

Progressive disease

IPF is a progressive disease, meaning the scarring in the lungs worsens over time, leading to increasingly severe symptoms.

No cure

There is currently no cure for IPF. However, medications and treatments are available that can help slow down the progression and improve quality of life.

Variable prognosis

Varying from person to person, some may experience a slow decline in lung function over several years, while others may have a more rapid progression.